Case Report

J Korean Hip Soc 2008; 20(3): 215-219

Published online September 1, 2008

© The Korean Hip Society

유전성 감각 및 자율신경병증 제 IV형 환자에서 발생한 고관절 후상방 탈구의 수술적 치료 - 증례 보고 -

조재호∙김상환∙김준용∙원예연

아주대학교 의과대학 정형외과학교실

Received: April 29, 2007; Revised: September 2, 2008; Accepted: September 3, 2008

Surgical Treatment of Posterosuperior Hip Dislocation in A Patient with Hereditary Sensory Autonomic Neuropathy Type IV - A Case Report -

Jae-ho Cho, M.D., Sang-hwan Kim, M.D., Joon-yong Kim, M.D., We-Yeon Won, M.D.

Department of Orthopaedic Surgery, Ajou University College of Medicine, Suwon, Korea

Correspondence to : 조재호
경기도 수원시 영통구 원천동 산5 아주대학교 의과대학 정형외과학교실
TEL: 82-31-219-5224
FAX: 82-31-219-5229
E-mail: cho@ajou.ac.kr

Received: April 29, 2007; Revised: September 2, 2008; Accepted: September 3, 2008

Abstract

A 4-year old female patient with a diagnosis of hereditary sensory autonomic neuropathy type IV (congenital insensitivity to pain with anhidrosis) since the age of 1 year, sustained a posterior hip dislocation. During her initial stay at the hospital, an attempt at manual reduction failed. Open reduction, capsulorrhaphy, and Salter operation were done at 36 days after the index dislocation. After the operation there was a 23-degree acetabular index, and there were several abnormal round whitish gray fibrous nodules. There was also severe wound discharge, skin abrasion, and erythema on the patient’s back and buttocks due to loss of protective sensation. After conservatively treating the wound and skin problems with prone positioning, we achieved a final acetabular index of 26 degrees. The patient did not have protective sensation in her hip joint. We were able to check for increasing instability after the index operation.

Keywords Hip dislocation, Hereditary sensory autonomic neuropathy type IV, Anhidrosis, Salter innominate osteotomy

Article

Case Report

J Korean Hip Soc 2008; 20(3): 215-219

Published online September 1, 2008 https://doi.org/10.5371/jkhs.2008.20.3.215

Copyright © The Korean Hip Society.

유전성 감각 및 자율신경병증 제 IV형 환자에서 발생한 고관절 후상방 탈구의 수술적 치료 - 증례 보고 -

조재호∙김상환∙김준용∙원예연

아주대학교 의과대학 정형외과학교실

Received: April 29, 2007; Revised: September 2, 2008; Accepted: September 3, 2008

Surgical Treatment of Posterosuperior Hip Dislocation in A Patient with Hereditary Sensory Autonomic Neuropathy Type IV - A Case Report -

Jae-ho Cho, M.D., Sang-hwan Kim, M.D., Joon-yong Kim, M.D., We-Yeon Won, M.D.

Department of Orthopaedic Surgery, Ajou University College of Medicine, Suwon, Korea

Correspondence to:조재호
경기도 수원시 영통구 원천동 산5 아주대학교 의과대학 정형외과학교실
TEL: 82-31-219-5224
FAX: 82-31-219-5229
E-mail: cho@ajou.ac.kr

Received: April 29, 2007; Revised: September 2, 2008; Accepted: September 3, 2008

Abstract

A 4-year old female patient with a diagnosis of hereditary sensory autonomic neuropathy type IV (congenital insensitivity to pain with anhidrosis) since the age of 1 year, sustained a posterior hip dislocation. During her initial stay at the hospital, an attempt at manual reduction failed. Open reduction, capsulorrhaphy, and Salter operation were done at 36 days after the index dislocation. After the operation there was a 23-degree acetabular index, and there were several abnormal round whitish gray fibrous nodules. There was also severe wound discharge, skin abrasion, and erythema on the patient’s back and buttocks due to loss of protective sensation. After conservatively treating the wound and skin problems with prone positioning, we achieved a final acetabular index of 26 degrees. The patient did not have protective sensation in her hip joint. We were able to check for increasing instability after the index operation.

Keywords: Hip dislocation, Hereditary sensory autonomic neuropathy type IV, Anhidrosis, Salter innominate osteotomy

H&P
Vol.36 No.1 Mar 01, 2024, pp. 1~75

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